As a rare condition, gastric volvulus occurs predominantly in neonates and infants.According to different etiologies, it may be classified into primary (about 30%) and secondary (about 70%) types.It is divided into three types based upon the rotation axis.Due to its multiple congenital associated malformations and non-specific clinical presentations, it is rather difficult to make a timely and accurate diagnosis, leading frequently to misdiagnosis and delayed diagnosis.Diagnostic delays of acute gastric volvulus result in such severe complications as gastric wall ischemia, necrosis, perforation, shock and even death in children.With the constant improvements of diagnostic technology, most children can be timely treated.However, a proper selection of surgical intervention has remained controversial.This review summarized the classification, diagnosis, treatments and outcomes of pediatric gastric volvulus.