Objective To summarize the clinical characteristics and treatment of spinal primitive neuroectodermal tumor.Methods Clinical data of 8 patients with spinal cord primitive neuroectodermal tumor were analyzed retrospectively. Results Microsurgery was performed in all of the 8 cases.Total removal was performed in 5 patients,subtotal in 1,most part in 1and partial in 1.During a follow - up of 1month to 24 months,Six patients died of disease,and 2 survived,mean follow up of survivor time is 12months. Conclusions Spinal primitive neuroectodermal tumor is rare,malignant,and poor prognoses tumor.The diagnosis of PNET is by means of routine pathology,immune histology and cytogenetic analysis.Although the best treatment is unavailable due to the limited data,surgery combined with radiotherapy or chemotherapy was recommended.