To analyze the clinical manifestations, imaging characteristics, treatment and pathological types of orbital rhabdomyosarcoma.

The clinical data of 36 eyes of 36 cases of orbital rhabdomyosarcoma from 1980 to 2018 in Second Hospital of Tianjin Medical University were analyzed retrospectively.

The ages ranged from 5 months to 14 years, with an average of (6.54±3.79) years. The tumors were most commonly located at supraorbital quadrant. Proptosis was the most common initial clinical sign. B-ultrasound examination showed low-echo or echoless areas. The color Doppler ultrasonography exploration showed arterial spectrum and blood flow was abundant. Twenty-eight patients underwent CT scans, the tumors showed soft tissue density, 6 cases showing bone destruction. Ten patients underwent MRI examinations, among which 8 cases displayed as iso- or slightly hypo-signal on T1WI, and hyper-signal on T2WI. In all the 36 cases, evisceration of orbital in 4 cases, and tumor was removed through anterior orbitotomy in 32 cases. The pathological examination showed that embryonal rhabdomyosarcoma accounted for 20 cases(55.6%), alveolar rhabdomyosarcoma and pleomorphic rhabdomyosarcoma accounted for 9 cases(25.0%)and 7 cases(19.4%) respectively.

Orbital rhabdomyosarcoma is a highly malignant tumor. Traditional B-ultrasound, CT, MRI combined with PET-CT and other imaging examinations can guide the diagnosis, treatment and monitoring of recurrence and metastasis.

Tumor, orbit; Rhabdomyosarcoma; Study, retrospective; Analysis, pathology