Guide to Analysis
Interpretation of " Idiopathic Pulmonary Fibrosis (an Update) and Progressive Pulmonary Fibrosis in Adults: An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline (2022 Edition)" : Identification and treatment of progressive pulmonary fibrosis
Mao Mengmeng, Guo Bingpeng, Han Qian
Published 2023-11-25
Cite as Int J Respir, 2023, 43(11): 1245-1250. DOI: 10.3760/cma.j.cn131368-20231013-00247
Abstract
In recent clinical trials, fibrotic interstitial lung disease (ILD) that shares the similar physiopathologic mechanism and behavior with those of idiopathic pulmonary fibrosis (IPF) have been uniformly termed as progressive fibrosing ILD (PF-ILD). However, there is no consensus on the definition and diagnostic criteria of PF-ILD." Idiopathic Pulmonary Fibrosis (an Update) and Progressive Pulmonary Fibrosis in Adults: An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline (2022 Edition)" unifies the process of ILD with progressive exacerbation of fibrosis other than idiopathic pulmonary fibrosis, and newly termed as progressive pulmonary fibrosis (PPF). They also clarify the diagnostic criteria, and anti-fibrosis treatment of PPF.This article thoroughly interprets this guideline for PPF.
Key words:
Lung diseases, interstitial; Progressive fibrosing interstitial lung disease; Progressive pulmonary fibrosis; Diagnostic criteria; Treatment recommendations
Contributor Information
Mao Mengmeng
Guangzhou Institute of Respiratory Health, State Key Laboratory of Respiratory Disease, National Clinical Research Center of Respiratory Disease, National Center for Respiratory Medicine, Department of Respiratory and Critical Diseases, the First Affiliated Hospital of Guangzhou Medical University, Guangzhou 510120, China
Guo Bingpeng
Guangzhou Institute of Respiratory Health, State Key Laboratory of Respiratory Disease, National Clinical Research Center of Respiratory Disease, National Center for Respiratory Medicine, Department of Respiratory and Critical Diseases, the First Affiliated Hospital of Guangzhou Medical University, Guangzhou 510120, China
Han Qian
Guangzhou Institute of Respiratory Health, State Key Laboratory of Respiratory Disease, National Clinical Research Center of Respiratory Disease, National Center for Respiratory Medicine, Department of Respiratory and Critical Diseases, the First Affiliated Hospital of Guangzhou Medical University, Guangzhou 510120, China
